Heyde’s Syndrome: A Case Report
DOI:
https://doi.org/10.56294/shp2024397Keywords:
gastrointestinal bleeding, severe aortic stenosisAbstract
Heyde’s syndrome is the association between aortic valve stenosis and gastrointestinal bleeding due to intestinal angiodysplasia. The pathophysiological basis of this syndrome appears to be an acquired deficiency of von Willebrand factor, leading to bleeding from angiodysplastic arteriovenous malformations. Treatment options include localization and cauterization of the bleeding sites, although this therapeutic approach is associated with a high recurrence rate. Aortic valve replacement appears to offer the best long-term resolution of bleeding and should be considered in most cases.
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Copyright (c) 2024 Aline Aparecida Pacheco , Analía Claudia Sabattini (Author)
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The article is distributed under the Creative Commons Attribution 4.0 License. Unless otherwise stated, associated published material is distributed under the same licence.
